| CASE REPORT |
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| Year : 2008 | Volume
: 3
| Issue : 2 | Page : 64-66 |
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Extramedullary paraspinal hematopoiesis in hereditary spherocytosis
P Gogia, R Goel, S Nayar
Department of Pulmonology, Jaipur Golden Hospital, New Delhi, India
Correspondence Address:
P Gogia
J-6/27 Rajouri Garden, New Delhi - 110 027
India
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/1817-1737.39640
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Hereditary spherocytosis (HS) is a common inherited hemolytic anemia due to red cell membrane defects. Extramedullary hematopoiesis is a compensatory response to insufficient bone marrow blood cell production. The preferred sites of extramedullary hematopoietic involvement are the spleen, liver and lymph nodes; but in HS, the posterior paravertebral mediastinum is also commonly involved. We report a case of a 50-year-old male who presented to us in respiratory distress and with bilateral paravertebral posterior mediastinal masses, which on trucut biopsy were found to be extra-hematopoietic masses; and the patient was found to have hereditary spherocytosis. |
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