CASE REPORT |
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Year : 2021 | Volume
: 16
| Issue : 3 | Page : 294-298 |
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Fatal rapidly progressive interstitial lung disease in a patient with amyopathic dermatomyositis
Abdullah Mobeireek1, Walter Conca1, Shamayel Mohammed2, Fahad AlObaid1, Mohammed AlHajji1
1 Department of Medicine, King Faisal Specialist Hospital and Research Centre, Riyadh, Saudi Arabia 2 Department of Laboratory Medicine and Pathology, King Faisal Specialist Hospital and Research Centre, Riyadh, Saudi Arabia
Correspondence Address:
Abdullah Mobeireek King Faisal Specialist Hospital and Research Centre, Department of Medicine, PO Box 3354 (MBC 46), Riyadh 11211 Saudi Arabia
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/atm.atm_739_20
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Interstitial lung disease (ILD) is a well-established common manifestation of idiopathic inflammatory myopathies. Yet, till now, the pathogenetic mechanisms are still poorly understood, classification is evolving and prognosis is variable. A refractory and rapidly progressive ILD (RPILD) that is associated with dermatomyositis (DM) with minimal muscle weakness and normal creatine kinase (termed clinically amyopathic DM) is increasingly being recognized, with more incidence in Asians. However, we are not aware of reports of the Arab region. Herein, we present a 38-year-old male with this condition that ended with a fatal outcome despite aggressive therapy, with a review of recent literature.
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